What is Rapunzel Syndrome? - An Unusual Trichobezoar Presentation in patients with or without History of Psychiatric Disorders. A Comprehensive Review.
"What is Rapunzel Syndrome"? - An Unusual Trichobezoar Presentation in patients with or without History of Psychiatric Disorders A Comprehensive Review.
The Rapunzel syndrome is an unusual form of trichobezoar found in patients with a history of psychiatric disorders, trichotillomania (habit of hair pulling) and trichophagia (morbid habit of chewing the hair), consequently developing gastric bezoars.
An unusual form of bezoar extending from the stomach to the small intestine or beyond has been described as Rapunzel syndrome.
Bezoars are concretions in the gastrointestinal tract that increase in size by continuous accumulation of non-absorbable food or fibers.
· Most bezoars in children are trichobezoars from swallowed hair from the head, dolls, or brushes.
· Trichobezoars typically cause abdominal pain and nausea, but can also present as an asymptomatic abdominal mass, progressing to abdominal obstruction and perforation.
· Trichobezoar with Rapunzel syndrome is an uncommon diagnosis in children with less than 40 cases reported.
It is predominantly found in emotionally disturbed or mentally retarded youngsters.
Thus an attempt has been made in this Booklet to describe this Syndrome and to present two cases with the discussions and relevant Illustrations to corroborate the occurrence of incidences.
Case Report no. (1) A 5-year-old, Female, born at 25weeks
gestation, youngest documented
patient with Rapunzel syndrome in
the USA, and
Case Report no. (2) A 22 years old, Female with a H/O
vomiting over the past three months
together with continuous, intense
epigastric pain.
…Dr. H. K. Saboowala.
M.B.(Bom) .M.R.S.H.(London)
The Rapunzel syndrome is an unusual form of trichobezoar found in patients with a history of psychiatric disorders, trichotillomania (habit of hair pulling) and trichophagia (morbid habit of chewing the hair), consequently developing gastric bezoars.
An unusual form of bezoar extending from the stomach to the small intestine or beyond has been described as Rapunzel syndrome.
Bezoars are concretions in the gastrointestinal tract that increase in size by continuous accumulation of non-absorbable food or fibers.
· Most bezoars in children are trichobezoars from swallowed hair from the head, dolls, or brushes.
· Trichobezoars typically cause abdominal pain and nausea, but can also present as an asymptomatic abdominal mass, progressing to abdominal obstruction and perforation.
· Trichobezoar with Rapunzel syndrome is an uncommon diagnosis in children with less than 40 cases reported.
It is predominantly found in emotionally disturbed or mentally retarded youngsters.
Thus an attempt has been made in this Booklet to describe this Syndrome and to present two cases with the discussions and relevant Illustrations to corroborate the occurrence of incidences.
Case Report no. (1) A 5-year-old, Female, born at 25weeks
gestation, youngest documented
patient with Rapunzel syndrome in
the USA, and
Case Report no. (2) A 22 years old, Female with a H/O
vomiting over the past three months
together with continuous, intense
epigastric pain.
…Dr. H. K. Saboowala.
M.B.(Bom) .M.R.S.H.(London)
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